Auditory agnosia is the term used by Pan et al (2004)
to describe the loss of speech understanding caused
by a cancerous growth into the inferior colliculi of the
patient described in their case report [1].  Auditory
agnosia, impairment in sound recognition with
seemingly adequate hearing, is according to Pan et
al, usually associated with lesions in the auditory
cortex; but they cite five earlier reports in which
agnosia for language was also caused by traumatic or
cancerous injury within the inferior colliculi [2-5].  
Additional case reports have been published by
Hoistad & Hain (2003), Kimiskidis et al (2004), and
Musiek et al (2004) [6-8].  Some of these papers cited
an earlier report by Howe and Miller (1975), who
found damage in the inferior colliculi after the patient's
death [9].  With MRI scanning, these small nuclei in
the midbrain can be clearly seen, and more reports of
functional loss following injury can be anticipated in
the future.

The inferior colliculi are more than simple way-stations
in the auditory pathway.  Auditory agnosia and loss of
speech understanding following bilateral lesions of the
inferior colliculi, in people who had previous full
command of language, indicates the importance of
these small nuclei.  How much more serious the effect
of damage in infancy must be, before the beginning of
language development.  The bilateral destruction of
the inferior colliculi caused by asphyxia at birth should
not be overlooked as a potential cause of
developmental language disorder.

In addition to awareness and attention, Fisch (1983)
discussed the role of the auditory system as the
evolutionary basis of language [11].  Language
continues to be viewed by many as a higher cognitive
function that (beyond the way a particular language is
learned by a young child) has little to do with hearing.  
Fisch, an audiologist, on the other hand maintained
that the raw material of language is sound and that it
is practically impossible to separate language from its
phonetic elements.  Speaking and hearing are a
major part of daily life, reading and writing much less
so.

According to Fisch (1983), in West European
languages there are on average four phonetic
elements per word and speech delivered at three
words per second can still be understood.  He pointed
out that the auditory system does not act just as a
cable but as a mechanism for transforming the signals
to be used by language centers of the cerebral
cortex.  Fisch further noted that in the auditory system
rapid extinction of signals increases the rate at which
sequential sounds can quickly be replaced, new
following old.

As described by Caspary et al. (1995), rapid
extinction of sounds is accomplished by inhibitory
neurotransmitters [11].  Speech sounds last about 40
milliseconds with rapid transitions from vowels to
plosives, with the sensation created by any one signal
not persisting long enough to interfere with
recognition of the next.

Phylogenetically the auditory system is a late
development [12].  Fisch suggested that the auditory
system is therefore more complex, with greater
metabolic activity, and is thus also more vulnerable to
unfavorable metabolic influences.  The auditory
system has clearly evolved beyond being a simple
alerting mechanism for visual attention.  The capacity
for language has developed along with, and as a
result of, an increasing capability to detect meaningful
short-lived changes in the acoustic environment.

Fisch noted that in birds, the auditory system ends in
the torus semicircularis, the auditory center within the
optic tectum.  Birds use auditory communication, for
which the system terminating in the tectum suffices
nicely.  Textbooks of comparative anatomy discuss
how in mammalian species the torus semicircularis of
lower vertebrates evolved into the paired inferior
colliculi, posterior to the superior (optic) colliculi [12].  
These are the corpora quadrigeminae of the midbrain
tectum, with connections to later evolutionary
structures of the thalamus and temporal and frontal
lobes of the cerebral cortex.
  1. Pan CL et al (2004) Auditory
    agnosia caused by a tectal
    germinoma.
  2. Meyer B et al (1996) Pure
    word deafness after
    resection of a tectal plate
    glioma with preservation of
    wave V of brain stem
    auditory evoked potentials.
  3. Johkura K et al (1998)
    Defective auditory
    recognition after small
    hemorrhage in the inferior
    colliculi.
  4. Masuda S et al (2000) Word
    deafness after resection of a
    pineal body tumor in the
    presence of normal wave
    latencies of the auditory
    brain stem response.
  5. Vitte E et al (2002) Midbrain
    deafness with normal
    brainstem auditory evoked
    potentials. (two case
    reports).
  6. Hoistad DL et al (2003)
    Central hearing loss with a
    bilateral inferior colliculus
    lesion.
  7. Kimiskidis VK et al (2004)
    Sensorineural hearing loss
    and word deafness caused
    by a mesencephalic lesion:
    clinicoelectrophysiologic
    correlations.
  8. Musiek FE et al (2004)
    Central deafness
    associated with a midbrain
    lesion.
  9. Howe JR, MillerCA (1975)
    Midbrain deafness following
    head injury.
  10. Fisch L (1983) Integrated
    development and maturation
    of the hearing system. A
    critical review article.
  11. Caspary DM et al. (1995)
    Central auditory aging: GABA
    changes in the inferior
    colliculus.
  12. Butler AB, Hodos W (1996)
    Comparative Vertebrate
    Neuroanatomy: Evolution
    and Adaptation
5 – Language and the inferior colliculi
References
Full References
top
  1. Pan CL, Kuo MF, Hsieh ST. Auditory agnosia caused by a tectal germinoma. Neurology.
    2004 Dec 28;63(12):2387-9.
  2. Meyer B, Kral T, Zentner J. (1996) Pure word deafness after resection of a tectal plate
    glioma with preservation of wave V of brain stem auditory evoked potentials. Journal of
    Neurology, Neurosurgery and Psychiatry. 61:423-4.
  3. Johkura K, Matsumoto S, Hasegawa O, Kuroiwa Y. (1998) Defective auditory recognition
    after small hemorrhage in the inferior colliculi. Journal of the Neurological Sciences.
    161:91-6
  4. Masuda S, Takeuchi K, Tsuruoka H, Ukai K, Sakakura Y. (2000) Word deafness after
    resection of a pineal body tumor in the presence of normal wave latencies of the
    auditory brain stem response. The Annals of otology, rhinology, and laryngology. 2000
    Dec;109(12 Pt 1):1107-12
  5. Vitte E, Tankéré F, Bernat I, Zouaoui A, Lamas G, Soudant J. Midbrain deafness with
    normal brainstem auditory evoked potentials. Neurology 2002;58:970–973.
  6. Hoistad DL, Hain TC (2003) Central hearing loss with a bilateral inferior colliculus
    lesion. Audiol Neurootol 2003 Mar-Apr; 8(2):111-223
  7. Kimiskidis VK, Lalaki P, Papagiannopoulos S, Tsitouridis I, Tolika T, Serasli E, Kazis D,
    Tsara V, Tsalighopoulos MG, Kazis A. Sensorineural hearing loss and word deafness
    caused by a mesencephalic lesion: clinicoelectrophysiologic correlations. Otol
    Neurotol. 2004 Mar;25(2):178-82.
  8. Musiek FE et al (2004) Central deafness associated with a midbrain lesion. J Am Acad
    Audiol 2004 feb; 15(2):133-151.
  9. Howe JR, Miller CA. Midbrain deafness following head injury. Neurology. 1975 Mar;25(3):
    286-9
  10. Fisch L (1983) Integrated development and maturation of the hearing system. A critical
    review article. British Journal of Audiology 17:137-154.
  11. Caspary DM, Milbrandt JC, Helfert RH (1995) Central auditory aging: GABA changes in
    the inferior colliculus.  Experimental Gerontology 30:349-360.
  12. Butler AB, Hodos W (1996) Comparative Vertebrate Neuroanatomy: Evolution and
    Adaptation New York:John Wiley.