5 - The broader autism phenotype
Asperger syndrome is a condition related to autism in
which minor motor impairments may be prominent.
Children with Asperger syndrome may be delayed in
learning to speak, but appear to develop full
command of language by age three or four. A small
percentage of children with autism develop normal
language past the age of four or five and are thus
referred to as children with "high functioning autism"
(HFA). As they grow older, children with high
functioning autism cannot easily be distinguished from
children with Asperger syndrome [1, 2]. Cederlund
and Gillberg (2004) studied 100 males with asperger
syndrome and concluded that Asperger syndrome is
not "mild" autism, but autism with mild (or lesser)
cognitive impairment [3].
Asperger syndrome is considered to be part of a
spectrum of autistic disorders. One difficulty with
thinking of Asperger syndrome as on a true spectrum
with autism (as defined by Kanner) is the motor
clumsiness often noted in children with Asperger
syndrome. However, autism and Asperger syndrome
resulting from trauma and hypoxia during a difficult
birth can be viewed as on a spectrum of impairment
resulting from varying degrees of involvement of
Myers' two patterns of perinatal brain damage:
1 - A brief episode of total oxygen cutoff would, as
in the case of the experimental moneys, result in
the brainstem pattern of damage with most severe
involvement of the inferior colliculi. A child so
afflicted would develop, as the monkeys did, with
some transient delay in motor development, which
would be optimistically dismissed by pediatricians
as totally within the normal variation of normal
limits. Concern might arise only when difficulties
with speech development become noticeable.
2 - A difficult, traumatic birth would more likely
result in Myers' second pattern of damage,
affecting the circulatory "watershed" areas of the
cortex, as well as the nuclei of the subcortical
motor system, which are metabolically somewhat
less active than the inferior colliculi. A final brief
period of total anoxia would involve the inferior
colliculi, but if not for quite as prolonged period of
time as the monkeys experienced, the impact on
learning to speak might be less severe.
Late language development is a problem for children
with Asperger's sysndrome. In their research on 100
males with Asperger's syndrome, Cederlund and
Gillberg noted, "Forty-five of 92 children (49%) for
whom fairly detailed data about early language
development were available, clearly did not have
normal language development at 2 years of age. It
cannot be concluded that the remainder had normal
language development."
Children with Asperger's syndrome are often reported
to have a superior command of language. They may
have an unusually large repertoire of learned
expressions, which as is often noted they may use
slightly or strangely tangential to the context or topic
of a conversation. Could this be the reason they are
also often viewed as good punners?
With severe involvement only of the inferior colliculus
(autism) on one end, and lesser involvement of the
inferior colliculus plus some impairment of motor
control (Asperger syndrome) at the other, the
spectrum could represent different degrees of the two
patterns of brain damage found by Myers. Cerebral
palsy is on this spectrum too, but with serious motor
handicaps and perhaps no language learning
difficulties at all. Unfortunately, brain damage most
often involves some degree of disability in every
functional sphere.
Even dyslexia should probably be investigated as a
language learning difficulty in which maturation of the
cross-modal tracts between the temporal, occipital,
parietal, and frontal lobes has not progressed
normally. How many different problems might be
related to the "trans-neuronal" disruption of brain
development observed by Faro and Windle as long
term outcomes of asphyxia at birth in monkeys.
Preventing oxygen insufficiency at birth needs to be a
priority. Optimism cannot overcome afflictions that
have for too long been viewed as mild or minimal in
young children. Outcomes in adulthood need to be
investigated. Oxygen deficiency at birth must be
taken seriously, because of the patterns of brain
damage known to result, and that these patterns
correspond to functional deficiencies of people with
autism spectrum disorders.
- Szatmari P et al. (1989)
Asperger's syndrome and
autism: comparison of early
history and outcome.
- Szatmari P et al. (1990)
Asperger's syndrome and
autism: neurocognitive
aspects.
- Cederlund M, Gillberg C
(2004) One hundred males
with Asperger syndrome: a
clinical study of background
and associated factors.
- Freitag CM et al. (2006)
Quantitative Assessment of
Neuromotor Function in
Adolescents with High
Functioning Autism and
Asperger Syndrome.
- Tani P et al. (2006). Clinical
neurological abnormalities in
young adults with Asperger
syndrome.
- Rinehart NJ et al. (2006) Gait
function in high-functioning
autism and Asperger's
disorder : evidence for basal-
ganglia and cerebellar
involvement?
- Gillberg C, Kadesjo B. (2003)
Why bother about
clumsiness? The
implications of having
developmental coordination
disorder (DCD).
- Hippler K, Klicpera C. (2003)
A retrospective analysis of
the clinical case records of
'autistic psychopaths'
diagnosed by Hans Asperger
and his team at the University
Children's Hospital, Vienna.
- Myers RE (1972) Two
patterns of perinatal brain
damage and their conditions
of occurrence.
- Faro MD, Windle WF (1969)
Transneuronal degeneration
in brains of monkeys
asphyxiated at birth.
- Szatmari P, Bartolucci G, Bremner R (1989) Asperger's syndrome and
autism: comparison of early history and outcome. Developmental Medicine
and Child Neurology 31:709-720.
- Szatmari P, Tuff L, Finlayson MA, Bartolucci G (1990) Asperger's
syndrome and autism: neurocognitive aspects. Journal of the American
Academy of Child and Adolescent Psychiatry 29:130-136.
- Cederlund M, Gillberg C (2004) One hundred males with Asperger
syndrome: a clinical study of background and associated factors.
Developmental Medicine & Child Neurology 46: 652-660.
- Freitag CM, Kleser C, Schneider M, von Gontard A. Quantitative
Assessment of Neuromotor Function in Adolescents with High Functioning
Autism and Asperger Syndrome. J Autism Dev Disord. 2006 Dec 15; [Epub
ahead of print]
- Tani P, Lindberg N, Appelberg B, Nieminen-von Wendt T, von Wendt L,
Porkka-Heiskanen T. Clinical neurological abnormalities in young adults
with Asperger syndrome. Psychiatry Clin Neurosci. 2006 Apr;60(2):253-5.
- Rinehart NJ, Tonge BJ, Bradshaw JL, Iansek R, Enticott PG, McGinley J.
Gait function in high-functioning autism and Asperger's disorder : evidence
for basal-ganglia and cerebellar involvement? Eur Child Adolesc
Psychiatry. 2006 Aug;15(5):256-64.
- Gillberg C, Kadesjo B. Why bother about clumsiness? The implications of
having developmental coordination disorder (DCD). Neural Plast. 2003;10
(1-2):59-68.
- Hippler K, Klicpera C. A retrospective analysis of the clinical case records
of 'autistic psychopaths' diagnosed by Hans Asperger and his team at the
University Children's Hospital, Vienna. Philos Trans R Soc Lond B Biol Sci.
2003 Feb 28;358(1430):291-301.
- Myers RE (1972) Two patterns of perinatal brain damage and their
conditions of occurrence. American Journal of Obstetrics and Gynecology
112:246-276
- Faro MD & Windle WF (1969) Transneuronal degeneration in brains of
monkeys asphyxiated at birth. Experimental Neurology 24:38-53.